Other less Frequent Pancreatic Tumors: What Should be Known about Clinical Features, Diagnosis and Treatment?
Rossana Percario, Paolo Panaccio, Fabio F. di Mola, Pierluigi Di Sebastiano, Tommaso Grottola
Acinar cell carcinoma of pancreas, a member of the large family of epithelial tumors, is defined by its morphological resemblance to acinar cells and production of pancreatic exocrine enzymes. Perivascular epithelial cell tumor of pancreas belongs to a family of mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epithelioid cells that includes angiomyolipoma, lymphangioma, and clear cell (sugar) tumors. The pancreas can be a site of hematological malignancies, including non-Hodgkin pancreatic lymphoma, post-transplant lymphoproliferative disorder, extraosseous multiple myeloma, myeloid sarcoma, and Castleman disease. Primary leiomyosarcoma of pancreas represents less than 0.1% of all pancreatic malignancies and can be considered an evolution of pancreatic leiomyoma. Squamous-lined cysts of pancreas are considered a minority of true cystic pancreatic lesions, which in their turn are members of the larger family of cystic lesions with pseudocysts and cystic neoplasms.
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