AJR 2003; 181:1049-1054.
Taouli B, Ghouadni M, Correas JM, Hammel P, Couvelard A, Richard S, Vilgrain V.
Von Hippel-Lindau disease is a rare autosomal dominant familial tumor syndrome associated with brain, retinal, and spinal cord hemangioblas-tomas; renal cysts and renal cell carcinoma; pheochromocytomas; and pancreatic cysts, pancreatic serous cystadenomas, and pancreatic neuroendocrine tumors. In this article, we show the major abdominal imaging features of von Hippel-Lindau disease using CT and MRI in a large series of more than 150 patients.